1. Gene
  2. Mccc2 - methylcrotonoyl-Coenzyme A carboxylase 2 (beta) Gene

Mccc2 - methylcrotonoyl-Coenzyme A carboxylase 2 (beta) Gene

Mus musculus

Also known as MCCB; 4930552N12Rik

Gene ID: 78038 | Gene type: protein coding

About Mccc2

Summary

Predicted to enable ATP binding activity and Ligase activity. Predicted to contribute to methylcrotonoyl-CoA carboxylase activity. Predicted to be involved in coenzyme A metabolic process and leucine catabolic process. Located in mitochondrion. Is expressed in metanephros and spinal cord. Human ortholog(s) of this gene implicated in 3-Methylcrotonyl-CoA carboxylase 2 deficiency and Mitochondrial Metabolism disease. Orthologous to human MCCC2 (methylcrotonyl-CoA carboxylase subunit 2). [provided by Alliance of Genome Resources, Apr 2022]

Mccc2 Products(1)

mRNA Protein Name
NM_030026.2 NP_084302.1 methylcrotonoyl-CoA carboxylase beta chain, mitochondrial
Protein Preferred Names Protein Names

methylcrotonoyl-CoA carboxylase beta chain, mitochondrial

3-methylcrotonyl-CoA carboxylase 2

3-methylcrotonyl-CoA carboxylase non-biotin-containing subunit

3-methylcrotonyl-CoA:carbon dioxide ligase subunit beta

MCCase subunit beta

Orthologs Information

Species Symbol Source ID
Homo sapiens Mccc2 NCBI NCBI:64087